RPGRIP1L anticorps (AA 41-140) (Biotin)

N° du produit ABIN1394251

Détail du produit anti-RPGRIP1L anticorps (Biotin)

Antigène: RPGRIP1L (RPGRIP1-Like (RPGRIP1L))

Épitope: AA 41-140

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp RPGRIP1L est conjugé à/à la Biotin

Application: Western Blotting (WB), ELISA, Immunohistochemistry (Frozen Sections) (IHC (fro)), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))

Homologie: Human,Mouse,Rat,Dog,Cow,Sheep,Pig,Horse,Rabbit,Guinea Pig

Purification: Purified by Protein A.

Immunogène: KLH conjugated synthetic peptide derived from human RPGRIP1L

Isotype: IgG

Information d'application

Indications d'application: WB 1:300-5000
IHC-P 1:200-400
IHC-F 1:100-500

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 μg/μL

Buffer: Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.

Agent conservateur: ProClin

Précaution d'utilisation: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C for 12 months.

Date de péremption: 12 months

Détails sur RPGRIP1L

Antigène: RPGRIP1L (RPGRIP1-Like (RPGRIP1L))

Autre désignation: RPGRIP1L (RPGRIP1L Produits)

Synonymes: anticorps si:ch1073-301i20.1, anticorps mks5, anticorps cors3, anticorps jbts7, anticorps nphp8, anticorps CORS3, anticorps FTM, anticorps JBTS7, anticorps MKS5, anticorps NPHP8, anticorps 1700047E16Rik, anticorps 4931437C01, anticorps Ftm, anticorps Nphp8, anticorps RGD1311099, anticorps RPGRIP1 like, anticorps RPGRIP1-like, anticorps Protein fantom, anticorps Rpgrip1-like, anticorps RPGRIP1L, anticorps rpgrip1l, anticorps mks-5, anticorps Rpgrip1l

Sujet:

Synonyms: CORS 3, CORS3, Fantom, FTM, JBTS 1, JBTS 7, JBTS1, JBTS7, Joubert syndrome 1, Joubert syndrome 7, Meckel syndrome, type 1, RPGRIP1-like, Meckel syndrome, type 5, MKS 5, MKS5, NPHP 8, NPHP8, nephrocystin 8, Protein fantom, Retinitis pigmentosa GTPase regulator interacting protein 1 like, RPGR interacting protein 1 like protein, RPGRIP1 like protein, FTM_HUMAN.

Background: RPGRIP1L is a 1,315 amino acid protein that belongs to the RPGRIP1 family and is thought to function in programmed cell death, craniofacial development and formation of the left-right axis. Existing as two alternatively spliced isoforms that localize to the cytoplasm, cytoskeleton, centrosome and cilium basal body, RPGRIP1L interacts with nephrocystin-4 and is moderately expressed in brain, retina and kidney. Containing two C2 domains, RPGRIP1L is encoded by a gene that maps to human chromosome 16q12.2. Defects in the gene encoding RPGRIP1L are the cause of Joubert syndrome type 7 (JBTS7), COACH syndrome (COACHS) and Meckel syndrome type 5 (MKS5).

Pathways: DNA Replication, Regulation of G-Protein Coupled Receptor Protein Signaling, Synthesis of DNA