IDUA anticorps (AA 101-200)

N° du produit ABIN1713845

Détail du produit anti-IDUA anticorps

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Épitope: AA 101-200

Reactivité: Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp IDUA est non-conjugé

Application: ELISA, Western Blotting (WB)

Réactivité croisée: Rat

Homologie: Human,Mouse

Purification: Purified by Protein A.

Immunogène: KLH conjugated synthetic peptide derived from human IDUA

Isotype: IgG

Information d'application

Indications d'application: WB 1:300-5000
ELISA 1:500-1000
IHC-P 1:200-400
IHC-F 1:100-500
IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200
ICC 1:100-500

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 μg/μL

Buffer: 0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.

Agent conservateur: ProClin

Précaution d'utilisation: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

Stock: 4 °C,-20 °C

Stockage commentaire: Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.

Date de péremption: 12 months

Détails sur IDUA

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Autre désignation: IDUA (IDUA Produits)

Synonymes: anticorps IDA, anticorps MPS1, anticorps 6030426D08, anticorps alpha-L-iduronidase, anticorps MGC80842, anticorps si:ch211-12e13.9, anticorps IDUA, anticorps iduronidase, alpha-L-, anticorps iduronidase, alpha-L- L homeolog, anticorps alpha-L-iduronidase, anticorps IDUA, anticorps Idua, anticorps idua.L, anticorps idua, anticorps LOC5564727

Sujet:

Synonyms: IDA, MPS1, Alpha-L-iduronidase, IDUA

Background: This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008].

ID gène: 3425

UniProt: P35475

Pathways: Glycosaminoglycan Metabolic Process