ACADL antibody can be used for detection of ACADL by ELISA at 1:312500. ACADL antibody can be used for detection of ACADL by western blot at 1 μg/mL, and HRP conjugated secondary antibody should be diluted 1:50,000 - 100,000.
Restrictions
For Research Use only
Format
Lyophilized
Reconstitution
Add 50 ?L of distilled water. Final antibody concentration is 1 mg/mL.
Concentration
1 mg/mL
Buffer
Antibody is lyophilized in PBS buffer with 2 % sucrose.
Conseil sur la manipulation
As with any antibody avoid repeat freeze-thaw cycles.
Stock
4 °C/-20 °C
Stockage commentaire
For short periods of storage (days) store at 4 °C. For longer periods of storage, store ACADL antibody at -20 °C.
Antigène
ACADL
(Acyl-CoA Dehydrogenase, Long Chain (ACADL))
anticorps zgc:55656, anticorps ACAD4, anticorps LCAD, anticorps ACOADA, anticorps AA960361, anticorps AU018452, anticorps C79855, anticorps acyl-CoA dehydrogenase long chain, anticorps acyl-CoA dehydrogenase, long chain, anticorps acyl-CoA dehydrogenase, long chain L homeolog, anticorps acyl-Coenzyme A dehydrogenase, long-chain, anticorps acadl, anticorps ACADL, anticorps Acadl, anticorps acadl.L
Sujet
ACADL belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta-oxidation of straight-chain fatty acid. Defects in this gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia.The protein encoded by this gene belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta-oxidation of straight-chain fatty acid. Defects in this gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia.