SLC25A19 anticorps (Middle Region)
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- Antigène Voir toutes SLC25A19 Anticorps
- SLC25A19 (Solute Carrier Family 25 (Mitochondrial Thiamine Pyrophosphate Carrier), Member 19 (SLC25A19))
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Épitope
- Middle Region
- Reactivité
- Humain, Souris, Rat, Lapin, Boeuf (Vache), Chien, Cobaye, Cheval, Saccharomyces cerevisiae, Mouton
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp SLC25A19 est non-conjugé
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Application
- Western Blotting (WB)
- Séquence
- VHRGSVYDAR EFSVHFVCGG LAACMATLTV HPVDVLRTRF AAQGEPKVYN
- Homologie
- Cow: 93%, Dog: 93%, Guinea Pig: 93%, Horse: 93%, Human: 100%, Mouse: 100%, Rabbit: 100%, Rat: 100%, Sheep: 93%, Yeast: 77%
- Attributs du produit
- This is a rabbit polyclonal antibody against SLC25A19. It was validated on Western Blot.
- Purification
- Affinity Purified
- Immunogène
- The immunogen is a synthetic peptide directed towards the middle region of human SLC25A19
- Top Product
- Discover our top product SLC25A19 Anticorps primaire
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- Indications d'application
- Optimal working dilutions should be determined experimentally by the investigator.
- Commentaires
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Antigen size: 320 AA
- Restrictions
- For Research Use only
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- Format
- Liquid
- Concentration
- Lot specific
- Buffer
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
- Agent conservateur
- Sodium azide
- Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Conseil sur la manipulation
- Avoid repeated freeze-thaw cycles.
- Stock
- -20 °C
- Stockage commentaire
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- Antigène
- SLC25A19 (Solute Carrier Family 25 (Mitochondrial Thiamine Pyrophosphate Carrier), Member 19 (SLC25A19))
- Autre désignation
- SLC25A19 (SLC25A19 Produits)
- Synonymes
- anticorps zgc:111878, anticorps 2900089E13Rik, anticorps DNC, anticorps MUP1, anticorps TPC, anticorps MCPHA, anticorps THMD3, anticorps THMD4, anticorps solute carrier family 25 member 19, anticorps solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19, anticorps Slc25a19, anticorps slc25a19, anticorps SLC25A19
- Sujet
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This gene encodes a mitochondrial protein that is a member of the solute carrier family. Although this protein was initially thought to be the mitochondrial deoxynucleotide carrier involved in the uptake of deoxynucleotides into the matrix of the mitochondria, further studies have demonstrated that this protein instead functions as the mitochondrial thiamine pyrophosphate carrier, which transports thiamine pyrophosphates into mitochondria. Mutations in this gene cause microcephaly, Amish type, a metabolic disease that results in severe congenital microcephaly, severe 2-ketoglutaric aciduria, and death within the first year. Multiple alternatively spliced variants, encoding the same protein, have been identified for this gene.
Alias Symbols: DNC, MCPHA, MUP1, TPC, THMD3, THMD4
Protein Interaction Partner: UBC,
Protein Size: 320 - Poids moléculaire
- 35 kDa
- ID gène
- 60386
- NCBI Accession
- NM_021734, NP_068380
- UniProt
- Q9HC21
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