FUCA1 anticorps (N-Term)
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- Antigène Voir toutes FUCA1 Anticorps
- FUCA1 (Fucosidase, alpha-L- 1, Tissue (FUCA1))
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Épitope
- N-Term
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Reactivité
- Humain, Souris, Rat, Boeuf (Vache), Chien, Lapin, Cobaye, Cheval, Porc
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp FUCA1 est non-conjugé
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Application
- Western Blotting (WB)
- Séquence
- PSPVSWNWNS KDVGPHRDLV GELGTALRKR NIRYGLYHSL LEWFHPLYLL
- Homologie
- Cow: 100%, Dog: 93%, Guinea Pig: 93%, Horse: 93%, Human: 100%, Mouse: 100%, Pig: 100%, Rabbit: 79%, Rat: 100%
- Attributs du produit
- This is a rabbit polyclonal antibody against FUCA1. It was validated on Western Blot using a cell lysate as a positive control.
- Purification
- Affinity Purified
- Immunogène
- The immunogen is a synthetic peptide directed towards the N terminal region of human FUCA1
- Top Product
- Discover our top product FUCA1 Anticorps primaire
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- Indications d'application
- Optimal working dilutions should be determined experimentally by the investigator.
- Commentaires
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Antigen size: 466 AA
- Restrictions
- For Research Use only
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- Format
- Liquid
- Concentration
- Lot specific
- Buffer
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
- Agent conservateur
- Sodium azide
- Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Conseil sur la manipulation
- Avoid repeated freeze-thaw cycles.
- Stock
- -20 °C
- Stockage commentaire
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- Antigène
- FUCA1 (Fucosidase, alpha-L- 1, Tissue (FUCA1))
- Autre désignation
- FUCA1 (FUCA1 Produits)
- Synonymes
- anticorps FUCA, anticorps FUCA1, anticorps 0610006A03Rik, anticorps 9530055J05Rik, anticorps Afuc, anticorps Fuca, anticorps fuca, anticorps fuca1, anticorps ATFUC1, anticorps F24D13.11, anticorps F24D13_11, anticorps alpha-L-fucosidase 1, anticorps wu:fb02a09, anticorps zgc:101116, anticorps alpha-L-fucosidase 1, anticorps fucosidase, alpha-L- 1, tissue, anticorps alpha-L-fucosidase 1 L homeolog, anticorps alpha-L-fucosidase 1, tandem duplicate 2, anticorps FUCA1, anticorps Fuca1, anticorps fuca1.L, anticorps fuca1, anticorps FUC1, anticorps LOC9317020, anticorps LOC100285202, anticorps fuca1.2
- Sujet
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Alpha-L-fucosidase (EC 3.2.1.51) is a lysosomal enzyme involved in the degradation of fucose-containing glycoproteins and glycolipids. At least 2 separate polymorphic alpha-L-fucosidases are recognized in man: that in tissues, FUCA1, which is deficient in fucosidosis, and that in plasma, FUCA2. Fucosidosis is an autosomal recessive lysosomal storage disease caused by defective alpha-L-fucosidase with accumulation of fucose in the tissues. Different phenotypes include clinical features such as neurologic deterioration, growth retardation, visceromegaly, and seizures in a severe early form, coarse facial features, angiokeratoma corporis diffusum, spasticity and delayed psychomotor development in a longer surviving form, and an unusual spondylometaphyseoepiphyseal dysplasia in yet another form.[supplied by OMIM]. Publication Note: This RefSeq record includes a subset of the publications that are available for this gene. Please see the Entrez Gene record to access additional publications.
Alias Symbols: FUCA
Protein Interaction Partner: PAXIP1, BARD1, APP, CUL3, VAV2, USP21, MARK2,
Protein Size: 466 - Poids moléculaire
- 54 kDa
- ID gène
- 2517
- NCBI Accession
- NM_000147, NP_000138
- UniProt
- P04066
- Pathways
- Glycosaminoglycan Metabolic Process
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