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BCKDHB anticorps (N-Term)

BCKDHB Reactivité: Humain, Rat, Porc, Lapin, Boeuf (Vache), Chien, Cheval WB Hôte: Lapin Polyclonal unconjugated
N° du produit ABIN2787755
  • Antigène Voir toutes BCKDHB Anticorps
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    Épitope
    • 8
    • 8
    • 7
    • 1
    • 1
    N-Term
    Reactivité
    Humain, Rat, Porc, Lapin, Boeuf (Vache), Chien, Cheval
    Hôte
    • 18
    Lapin
    Clonalité
    • 18
    Polyclonal
    Conjugué
    • 8
    • 2
    • 2
    • 2
    • 2
    • 2
    Cet anticorp BCKDHB est non-conjugé
    Application
    • 18
    • 14
    • 14
    • 14
    • 13
    • 5
    • 3
    • 1
    Western Blotting (WB)
    Séquence
    GFLHPAATVE DAAQRRQVAH FTFQPDPEPR EYGQTQKMNL FQSVTSALDN
    Homologie
    Cow: 93%, Dog: 93%, Horse: 93%, Human: 100%, Pig: 86%, Rabbit: 93%, Rat: 79%
    Attributs du produit
    This is a rabbit polyclonal antibody against BCKDHB. It was validated on Western Blot.
    Purification
    Affinity Purified
    Immunogène
    The immunogen is a synthetic peptide directed towards the N-terminal region of Human BCKDHB
    Top Product
    Discover our top product BCKDHB Anticorps primaire
  • Restrictions
    For Research Use only
  • Format
    Liquid
    Concentration
    1 mg/mL
    Buffer
    Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
    Agent conservateur
    Sodium azide
    Précaution d'utilisation
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Conseil sur la manipulation
    Avoid repeat freeze-thaw cycles.
    Stock
    -20 °C
    Stockage commentaire
    For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
  • Antigène
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    Autre désignation
    BCKDHB (BCKDHB Produits)
    Synonymes
    anticorps zgc:158777, anticorps BCKDHB, anticorps E1B, anticorps dJ279A18.1, anticorps branched chain keto acid dehydrogenase E1, beta polypeptide, anticorps branched chain keto acid dehydrogenase E1 subunit beta, anticorps branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog, anticorps branched chain ketoacid dehydrogenase E1, beta polypeptide, anticorps BCKDHB, anticorps bckdhb, anticorps bckdhb.S, anticorps Bckdhb
    Sujet
    Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3' non-coding regions, but encoding the same isoform.
    Protein Interaction Partner: CUL3, BCKDHA,
    Protein Size: 218
    Poids moléculaire
    23 kDa
    ID gène
    594
    UniProt
    Q5T2J3
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