AMMECR1 anticorps (C-Term)
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- Antigène Voir toutes AMMECR1 Anticorps
- AMMECR1 (Alport Syndrome, Mental Retardation, Midface Hypoplasia and Elliptocytosis Chromosomal Region Gene 1 (AMMECR1))
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Épitope
- C-Term
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Reactivité
- Humain, Souris, Boeuf (Vache), Chien, Cobaye, Cheval, Lapin, Rat, Poisson zèbre (Danio rerio)
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp AMMECR1 est non-conjugé
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Application
- Western Blotting (WB)
- Séquence
- DHIQTIDSLL RKGGYKAPIT NEFRKTIKLT RYRSEKMTLS YAEYLAHRQH
- Homologie
- Cow: 100%, Dog: 100%, Guinea Pig: 100%, Horse: 100%, Human: 100%, Mouse: 100%, Rabbit: 100%, Rat: 100%, Zebrafish: 100%
- Attributs du produit
- This is a rabbit polyclonal antibody against AMMECR1. It was validated on Western Blot.
- Purification
- Affinity Purified
- Immunogène
- The immunogen is a synthetic peptide directed towards the C-terminal region of Human AMMECR1
- Top Product
- Discover our top product AMMECR1 Anticorps primaire
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- Indications d'application
- Optimal working dilutions should be determined experimentally by the investigator.
- Commentaires
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Antigen size: 296 AA
- Restrictions
- For Research Use only
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- Format
- Liquid
- Concentration
- Lot specific
- Buffer
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
- Agent conservateur
- Sodium azide
- Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Conseil sur la manipulation
- Avoid repeated freeze-thaw cycles.
- Stock
- -20 °C
- Stockage commentaire
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- Antigène
- AMMECR1 (Alport Syndrome, Mental Retardation, Midface Hypoplasia and Elliptocytosis Chromosomal Region Gene 1 (AMMECR1))
- Autre désignation
- AMMECR1 (AMMECR1 Produits)
- Synonymes
- anticorps ammerc1, anticorps MGC84095, anticorps AMMECR1, anticorps Ammecr1, anticorps AMMERC1, anticorps 6230420G18Rik, anticorps Alport syndrome, mental retardation, midface hypoplasia and elliptocytosis chromosomal region gene 1 L homeolog, anticorps Alport syndrome, mental retardation, midface hypoplasia and elliptocytosis chromosomal region gene 1, anticorps ammecr1.L, anticorps AMMECR1, anticorps Ammecr1, anticorps ammecr1
- Sujet
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The exact function of this gene is not known, however, submicroscopic deletion of the X chromosome including this gene, COL4A5, and FACL4 genes, result in a contiguous gene deletion syndrome, the AMME complex (Alport syndrome, mental retardation, midface hypoplasia, and elliptocytosis). Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
Alias Symbols: AMMERC1
Protein Interaction Partner: ADAMTSL4, RBPMS, CALCOCO2, ELAVL1, UBC,
Protein Size: 296 - Poids moléculaire
- 31 kDa
- ID gène
- 9949
- NCBI Accession
- NM_001025580, NP_001020751
- UniProt
- Q9Y4X0
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