BLOC1S3 anticorps (N-Term)

N° du produit ABIN2790099

Détail du produit anti-BLOC1S3 anticorps

Antigène: BLOC1S3 (Biogenesis of Lysosomal Organelles Complex-1, Subunit 3 (BLOC1S3))

Épitope: N-Term

Reactivité: Humain, Souris, Rat, Boeuf (Vache), Mouton, Chien, Poisson zèbre (Danio rerio), Chévre, Cobaye, Cheval

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp BLOC1S3 est non-conjugé

Application: Western Blotting (WB)

Séquence: RGRPTGLRVA GEAAETDSEP EPEPEPTAAP RDLPPLVVQR ESAEEAWGTE

Homologie: Cow: 93%, Dog: 86%, Goat: 79%, Guinea Pig: 86%, Horse: 79%, Human: 100%, Mouse: 100%, Rat: 100%, Sheep: 79%, Zebrafish: 79%

Attributs du produit: This is a rabbit polyclonal antibody against BLOC1S3. It was validated on Western Blot.

Purification: Affinity Purified

Information d'application

Indications d'application: Optimal working dilutions should be determined experimentally by the investigator.

Commentaires:

Antigen size: 202 AA

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: Lot specific

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeated freeze-thaw cycles.

Stock: -20 °C

Stockage commentaire: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Détails sur BLOC1S3

Antigène: BLOC1S3 (Biogenesis of Lysosomal Organelles Complex-1, Subunit 3 (BLOC1S3))

Autre désignation: BLOC1S3 (BLOC1S3 Produits)

Synonymes: anticorps BLOS3, anticorps HPS8, anticorps RP, anticorps BC043666, anticorps Blos3, anticorps E230011O18, anticorps rp, anticorps biogenesis of lysosomal organelles complex 1 subunit 3, anticorps biogenesis of lysosomal organelles complex-1, subunit 3, anticorps BLOC1S3, anticorps Bloc1s3

Sujet: This gene encodes a protein that is a component of the BLOC1 multi-subunit protein complex. This complex is necessary for the biogenesis of specialized organelles of the endosomal-lysosomal system, including platelet dense granules and melanosomes. Mutations in this gene cause Hermansky-Pudlak syndrome 8, a disease characterized by lysosomal storage defects, bleeding due to platelet storage pool deficiency, and oculocutaneous albinism.
Alias Symbols: BLOS3, FLJ26641, FLJ26676, HPS8, RP
Protein Interaction Partner: BLOC1S3, BLOC1S2, BLOC1S1, DTNBP1, BLOC1S5, BLOC1S6, SNAPIN,
Protein Size: 202

Poids moléculaire: 21 kDa

ID gène: 388552

NCBI Accession: NM_212550, NP_997715

UniProt: Q6QNY0