IVD anticorps (AA 201-300) (AbBy Fluor® 594)

N° du produit ABIN2803373

Détail du produit anti-IVD anticorps (AbBy Fluor® 594)

Antigène: IVD (Isovaleryl-CoA Dehydrogenase (IVD))

Épitope: AA 201-300

Reactivité: Humain, Souris

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp IVD est conjugé à/à la AbBy Fluor® 594

Application: Western Blotting (WB), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))

Réactivité croisée: Humain, Souris

Homologie: Rat,Dog,Cow,Sheep,Pig,Horse,Rabbit

Purification: Purified by Protein A.

Immunogène: KLH conjugated synthetic peptide derived from human IVD

Isotype: IgG

Information d'application

Indications d'application: IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 μg/μL

Buffer: Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.

Agent conservateur: ProClin

Précaution d'utilisation: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Date de péremption: 12 months

Détails sur IVD

Antigène: IVD (Isovaleryl-CoA Dehydrogenase (IVD))

Autre désignation: IVD (IVD Produits)

Synonymes: anticorps 1300016K07Rik, anticorps 6720455E18Rik, anticorps AI463340, anticorps ACAD2, anticorps ATIVD, anticorps ISOVALERYL-COA-DEHYDROGENASE, anticorps ISOVALERYL-COA-DEHYDROGENASE PRECURSOR, anticorps IVDH, anticorps isovaleryl-CoA-dehydrogenase, anticorps isovaleryl coenzyme A dehydrogenase, anticorps isovaleryl-CoA dehydrogenase, anticorps isovaleryl-CoA-dehydrogenase, anticorps Ivd, anticorps IVD

Sujet:

Synonyms: ACAD2, Isovaleryl-CoA dehydrogenase, mitochondrial, IVD

Background: Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Apr 2009]

ID gène: 3712

UniProt: P26440

Pathways: Monocarboxylic Acid Catabolic Process