LRPPRC anticorps (AbBy Fluor® 594)

N° du produit ABIN2803844

Détail du produit anti-LRPPRC anticorps (AbBy Fluor® 594)

Antigène: LRPPRC (Leucine-Rich PPR-Motif Containing (LRPPRC))

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp LRPPRC est conjugé à/à la AbBy Fluor® 594

Application: Western Blotting (WB), Immunofluorescence (Paraffin-embedded Sections) (IF (p))

Réactivité croisée: Humain, Souris, Rat

Purification: Purified by Protein A.

Immunogène: KLH conjugated synthetic peptide derived from human LRP130

Isotype: IgG

Information d'application

Indications d'application: IF(IHC-P) 1:50-200

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 μg/μL

Buffer: Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.

Agent conservateur: ProClin

Précaution d'utilisation: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Date de péremption: 12 months

Détails sur LRPPRC

Antigène: LRPPRC (Leucine-Rich PPR-Motif Containing (LRPPRC))

Autre désignation: LRP130 (LRPPRC Produits)

Synonymes: anticorps CLONE-23970, anticorps GP130, anticorps LRP130, anticorps LSFC, anticorps Lrp157, anticorps 3110001K13Rik, anticorps C76645, anticorps Gp130, anticorps Lrp130, anticorps Lsfc, anticorps leucine rich pentatricopeptide repeat containing, anticorps leucine-rich pentatricopeptide repeat containing, anticorps leucine-rich PPR-motif containing, anticorps LRPPRC, anticorps Lrpprc

Sujet:

Synonyms: LRPPRC, 130 kDa leucine-rich protein, GP130, Leucine-rich PPR-mot containing protein, LRP 130, LPPRC_HUMAN.

Background: Leucine-rich protein (LRP130) is a cytoplasmic mRNA-binding protein likely to be involved in the processing of mitochondrial DNA transcripts. Defects in the LRPPRC gene that encodes LRP130 result in the French-Canadian type of Leigh syndrome, a severe neurological disorder characterized by lesions in the subcortical region of the brain. LRP130 also interacts with the low-affinity receptor for leukemia inhibitory factor to produce an intracelluar signal cascade.