HPS3 anticorps (C-Term)
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- Antigène Voir toutes HPS3 Anticorps
- HPS3 (Hermansky-Pudlak Syndrome 3 (HPS3))
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Épitope
- C-Term
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Reactivité
- Humain
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Hôte
- Chèvre
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp HPS3 est non-conjugé
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Application
- Western Blotting (WB)
- Séquence
- PYLLYCSRKK PLT
- Specificité
- This antibody recognizes HPS3/Cocoa
- Réactivité croisée (Details)
- Species reactivity (tested):Human.
- Purification
- Ammonium Sulphate Precipitation followed by antigen Affinity Chromatography using the immunizing peptide.
- Immunogène
- Peptide from the C Terminus of the protein sequence according to NP_115759
- Top Product
- Discover our top product HPS3 Anticorps primaire
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- Indications d'application
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Peptide ELISA: > 1/32,000. Western Blot: 1-3 μg/mL. Detects a band of Approx 110 kDa in A431 cell lysate(Predicted Molecular Weight: 114 kDa).
Other applications not tested.
Optimal dilutions are dependent on conditions and should be determined by the user. - Restrictions
- For Research Use only
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- Concentration
- 0.5 mg/mL
- Buffer
- Tris saline, pH 7.3 containing 0.02 % Sodium Azide as preservative and 0.5 % BSA as stabilizer.
- Agent conservateur
- Sodium azide
- Précaution d'utilisation
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Conseil sur la manipulation
- Avoid repeated freezing and thawing.
- Stock
- -20 °C
- Stockage commentaire
- Store the antibody (in aliquots) at -20 °C.
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- Antigène
- HPS3 (Hermansky-Pudlak Syndrome 3 (HPS3))
- Autre désignation
- HPS3 (HPS3 Produits)
- Synonymes
- anticorps SUTAL, anticorps HPS3, anticorps coa, anticorps HPS3, biogenesis of lysosomal organelles complex 2 subunit 1, anticorps HPS3, biogenesis of lysosomal organelles complex 2 subunit 1 L homeolog, anticorps Hermansky-Pudlak syndrome 3, anticorps HPS3, anticorps hps3.L, anticorps Hps3
- Sujet
- HPS3 is involved in early stages of melanosome biogenesis and maturation. Defects in HPS3 are the cause of the cocoa (coa) mutant, and of Hermansky-Pudlak syndrome type 3 (HPS3). HPS3 is an autosomal recessive disorder, characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.Synonyms: Hermansky-Pudlak syndrome 3
- ID gène
- 84343
- NCBI Accession
- NP_115759
- UniProt
- Q969F9
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