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GNS anticorps (AA 174-203)

GNS Reactivité: Humain WB, IHC (p) Hôte: Lapin Polyclonal RB19340 unconjugated
N° du produit ABIN390494
  • Antigène Voir toutes GNS Anticorps
    GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
    Épitope
    • 15
    • 3
    • 3
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 174-203
    Reactivité
    • 32
    • 8
    • 6
    • 3
    • 3
    • 3
    • 3
    • 3
    • 2
    • 2
    • 2
    • 2
    Humain
    Hôte
    • 29
    • 2
    • 1
    Lapin
    Clonalité
    • 32
    Polyclonal
    Conjugué
    • 18
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    Cet anticorp GNS est non-conjugé
    Application
    • 16
    • 13
    • 13
    • 10
    • 6
    • 4
    • 3
    • 2
    • 1
    • 1
    • 1
    Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    Homologie
    B, M
    Purification
    This antibody is prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis against PBS.
    Immunogène
    This GNS antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 174-203 amino acids from the Central region of human GNS.
    Clone
    RB19340
    Isotype
    Ig Fraction
    Top Product
    Discover our top product GNS Anticorps primaire
  • Indications d'application
    WB: 1:1000. IHC-P: 1:50~100
    Restrictions
    For Research Use only
  • Format
    Liquid
    Buffer
    Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.
    Agent conservateur
    Sodium azide
    Précaution d'utilisation
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Stock
    4 °C,-20 °C
    Stockage commentaire
    Maintain refrigerated at 2-8 °C for up to 6 months. For long term storage store at -20 °C in small aliquots to prevent freeze-thaw cycles.
    Date de péremption
    6 months
  • Antigène
    GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
    Autre désignation
    GNS (GNS Produits)
    Synonymes
    anticorps G6S, anticorps 2610016K11Rik, anticorps AU042285, anticorps C87209, anticorps N28088, anticorps NV14559, anticorps N-acetylglucosamine-6-sulfatase, anticorps zgc:114066, anticorps gns, anticorps wu:fi20h10, anticorps zgc:55370, anticorps glucosamine (N-acetyl)-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase S homeolog, anticorps glucosamine (N-acetyl)-6-sulfatase a, anticorps N-acetylglucosamine-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b, anticorps GNS, anticorps Gns, anticorps gns.S, anticorps gns, anticorps gnsa, anticorps CpipJ_CPIJ000745, anticorps Sros_7372, anticorps VDBG_04409, anticorps Halhy_3165, anticorps gnsb
    Sujet
    GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
    Poids moléculaire
    62082
    ID gène
    2799
    NCBI Accession
    NP_002067
    UniProt
    P15586
    Pathways
    Glycosaminoglycan Metabolic Process
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