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GLA anticorps (C-Term)

GLA Reactivité: Souris WB Hôte: Lapin Polyclonal unconjugated
N° du produit ABIN4886604
  • Antigène Voir toutes GLA Anticorps
    GLA (Galactosidase, alpha (GLA))
    Épitope
    • 16
    • 5
    • 5
    • 4
    • 4
    • 4
    • 4
    • 4
    • 3
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    AA 218-275, C-Term
    Reactivité
    • 57
    • 30
    • 20
    • 4
    • 4
    • 4
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    Souris
    Hôte
    • 68
    • 8
    • 2
    Lapin
    Clonalité
    • 71
    • 7
    Polyclonal
    Conjugué
    • 34
    • 13
    • 12
    • 7
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    Cet anticorp GLA est non-conjugé
    Application
    • 64
    • 34
    • 17
    • 17
    • 13
    • 13
    • 8
    • 7
    • 6
    • 6
    • 4
    • 3
    • 3
    • 1
    Western Blotting (WB)
    Fonction
    Rabbit IgG polyclonal antibody for Alpha-galactosidase A(Gla) detection. Tested with WB in mouse.
    Séquence
    DIQYYCNHWR NFDDVYDSWE SIKNILSWTV VYQKEIVEVA
    Réactivité croisée (Details)
    No cross reactivity with other proteins.
    Attributs du produit
    Rabbit IgG polyclonal antibody for Alpha-galactosidase A(Gla) detection. Tested with WB in mouse.
    Gene Name: galactosidase, alpha
    Protein Name: Alpha-galactosidase A
    Purification
    Immunogen affinity purified.
    Immunogène
    A synthetic peptide corresponding to a sequence at the C-terminus of mouse Gla (218-275aa DIQYYCNHWRNFDDVYDSWESIKNILSWTVVYQKEIVEVA), different from the related human sequence by fifteen amino acids.
    Isotype
    IgG
    Top Product
    Discover our top product GLA Anticorps primaire
  • Indications d'application
    WB: Concentration: 0.1-0.5 μg/mL, Tested Species: Mouse
    Notes: Tested Species: Species with positive results.
    Other applications have not been tested. Optimal dilutions should be determined by end users.
    Commentaires

    Antibody can be supported by chemiluminescence kit ABIN921124 in WB.

    Restrictions
    For Research Use only
  • Format
    Lyophilized
    Reconstitution
    Add 0.2 mL of distilled water will yield a concentration of 500 μg/mL.
    Concentration
    500 μg/mL
    Buffer
    Each vial contains 5 mg BSA, 0.9 mg NaCl, 0.2 mg Na2HPO4, 0.05 mg Sodium azide.
    Agent conservateur
    Sodium azide
    Précaution d'utilisation
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Conseil sur la manipulation
    Avoid repeated freezing and thawing.
    Stock
    4 °C/-20 °C
    Stockage commentaire
    At -20°C for one year. After reconstitution, at 4°C for one month.
    It can also be aliquotted and stored frozen at -20 °C for a longer time. Avoid repeated freezing and thawing.
  • Antigène
    GLA (Galactosidase, alpha (GLA))
    Autre désignation
    Gla (GLA Produits)
    Synonymes
    anticorps GALA, anticorps Ags, anticorps zgc:101584, anticorps MGC130872, anticorps SMU.877, anticorps SCF11.21, anticorps AO090005000217, anticorps alpha-GAL, anticorps galactosidase alpha, anticorps galactosidase, alpha, anticorps galactosidase alpha S homeolog, anticorps alpha-galactosidase, anticorps aga, anticorps alpha-galactosidase A, anticorps GLA, anticorps Gla, anticorps gla, anticorps gla.S, anticorps agaN, anticorps aga, anticorps agaL, anticorps SCO0541, anticorps rafA, anticorps melA, anticorps galA, anticorps ANI_1_2528074, anticorps ANI_1_1502124, anticorps AOR_1_390174, anticorps CpipJ_CPIJ002066, anticorps MCYG_00962, anticorps MCYG_00791, anticorps Tsp_02909, anticorps Tsp_02508
    Sujet
    Alpha-galactosidase is a glycoside hydrolase enzyme that encoded by the GLA gene. This gene is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.

    Synonyms: Ags | Agalsidase alfa | Alpha D galactosidase A | Alpha gal A | GALA | Galactosidase, alpha | GLA | GLA protein | Melibiase | P06280
    ID gène
    11605
    UniProt
    P51569
    Pathways
    SARS-CoV-2 Protein Interactome
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