GMPPB anticorps (AA 111-210) (AbBy Fluor® 750)
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- Antigène Voir toutes GMPPB Anticorps
- GMPPB (GDP-Mannose Pyrophosphorylase B (GMPPB))
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Épitope
- AA 111-210
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Reactivité
- Humain
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp GMPPB est conjugé à/à la AbBy Fluor® 750
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Application
- Western Blotting (WB), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))
- Homologie
- Human,Mouse,Rat,Cow,Sheep,Pig,Horse,Rabbit
- Purification
- Purified by Protein A.
- Immunogène
- KLH conjugated synthetic peptide derived from human GMPPB
- Isotype
- IgG
- Top Product
- Discover our top product GMPPB Anticorps primaire
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- Indications d'application
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IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200 - Restrictions
- For Research Use only
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- Format
- Liquid
- Concentration
- 1 μg/μL
- Buffer
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
- Agent conservateur
- ProClin
- Précaution d'utilisation
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- Stock
- -20 °C
- Stockage commentaire
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
- Date de péremption
- 12 months
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- Antigène
- GMPPB (GDP-Mannose Pyrophosphorylase B (GMPPB))
- Autre désignation
- GMPPB (GMPPB Produits)
- Synonymes
- anticorps MDDGA14, anticorps MDDGB14, anticorps MDDGC14, anticorps AI317178, anticorps E430010H19, anticorps RGD1560458, anticorps gmppl, anticorps zgc:92026, anticorps GMPPB, anticorps gmppb, anticorps gmppb-a, anticorps gmppb-b, anticorps GDP-mannose pyrophosphorylase B, anticorps GDP-mannose pyrophosphorylase B L homeolog, anticorps GDP-mannose pyrophosphorylase B S homeolog, anticorps GMPPB, anticorps Gmppb, anticorps gmppb, anticorps LOAG_13550, anticorps gmppb.L, anticorps gmppb.S
- Sujet
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Synonyms: GDP mannose pyrophosphorylase B, GDP-mannose pyrophosphorylase B, GMPPB, GMPPB_HUMAN, GTP-mannose-1-phosphate guanylyltransferase beta, KIAA1851, Mannose 1 phosphate guanylyltransferase, Mannose-1-phosphate guanyltransferase beta.
Background: GMPPB is a 360 amino acid protein that belongs to the transferase hexapeptide repeat family and is involved in protein modification pathways. Functioning as a GDP-mannose pyrophosphorylase, GMPPB enzymatically catalyzes the conversion of mannose-1-phosphate and GTP to GDP-mannose and a free phosphate, a reaction that is involved in the production of N-linked oligosaccharides. Defects in the gene encoding GMPPB that cause errors in the glycosylation pathway may lead to congenital disorders of glycosylation (CDG). CDGs are multisystemic diseases that often involve both the central and peripheral nervous systems and are often characterized by endocrine and coagulation disorders. GMPPB is expressed as two isoforms due to alternative splicing events.
- ID gène
- 29925
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