Dysferlin anticorps (C-Term)
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- Antigène Voir toutes Dysferlin (DYSF) Anticorps
- Dysferlin (DYSF)
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Épitope
- C-Term
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Reactivité
- Humain
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp Dysferlin est non-conjugé
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Application
- Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
- Specificité
- This antibody reacts to Dysferlin, Limb Girdle Muscular Dystrophy 2b (AUTOSOMAL RECESSIVE) (DYSF).
- Purification
- Immunoaffinity Chromatography
- Immunogène
- A synthetic peptide corresponding to C-terminal of human Dysferlin Genename: DYSF
- Isotype
- IgG
- Top Product
- Discover our top product DYSF Anticorps primaire
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- Indications d'application
- Optimal working dilution should be determined by the investigator.
- Restrictions
- For Research Use only
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- Buffer
- 10 mM PBS, pH 7.4 containing BSA as stabilizer and 0,09 % sodium azide as preservative
- Agent conservateur
- Sodium azide
- Précaution d'utilisation
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Stock
- 4 °C
- Stockage commentaire
- Store the antibody undiluted at 2-8 °C. DO NOT FREEZE!
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- Antigène
- Dysferlin (DYSF)
- Autre désignation
- Dysferlin (DYSF Produits)
- Synonymes
- anticorps DYSF, anticorps fb73b05, anticorps wu:fb73b05, anticorps si:rp71-50c18.1, anticorps DKFZp459E1226, anticorps 2310004N10Rik, anticorps AI604795, anticorps D6Pas3, anticorps mFLJ00175, anticorps FER1L1, anticorps LGMD2B, anticorps MMD1, anticorps dysferlin, anticorps dysferlin, limb girdle muscular dystrophy 2B (autosomal recessive), anticorps myoferlin, anticorps DYSF, anticorps dysf, anticorps LOC589501, anticorps Dysf
- Sujet
- Dysferlin is the protein product of the 2p13 gene that is defective in patients with Limb-Girdle Muscular Dystrophy type 2B (LGMD2B) and Miyoshi Myopathy (MM). Dysferlin is normally localized to the muscle plasma membrane. In patients with LGMD2B and MM, immunoreactivity to dysferlin is severely reduced or lost, depending on the type of mutation. This antibody is used for the characterization of LGMD2B and MM.Synonyms: DYSF, Dystrophy-associated fer-1-like protein, FER1L1, Fer-1-like protein 1
- ID gène
- 8291
- NCBI Accession
- NP_001123927
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