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GNS anticorps (AA 238-355)

GNS Reactivité: Humain, Souris, Rat WB, ELISA Hôte: Lapin Polyclonal unconjugated
N° du produit ABIN5693115
  • Antigène Voir toutes GNS Anticorps
    GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
    Épitope
    • 15
    • 3
    • 3
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 238-355
    Reactivité
    • 32
    • 7
    • 5
    • 3
    • 3
    • 3
    • 3
    • 3
    • 2
    • 2
    • 2
    • 2
    Humain, Souris, Rat
    Hôte
    • 29
    • 2
    • 1
    Lapin
    Clonalité
    • 32
    Polyclonal
    Conjugué
    • 18
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    Cet anticorp GNS est non-conjugé
    Application
    • 16
    • 13
    • 13
    • 9
    • 6
    • 5
    • 3
    • 2
    • 1
    • 1
    • 1
    Western Blotting (WB), ELISA
    Marque
    Picoband™
    Réactivité croisée (Details)
    No cross reactivity with other proteins.
    Attributs du produit
    Rabbit IgG polyclonal antibody for GNS detection. Tested with WB, Direct ELISA in Human,Mouse,Rat.
    Immunogène
    E. coli-derived human GNS recombinant protein (Position: W238-R355).
    Top Product
    Discover our top product GNS Anticorps primaire
  • Indications d'application

    Recommended Detection Systems: Enhanced Chemiluminescent Kit with anti-Rabbit IgG (ABIN921124) for Western blot.

    Application Details: Western blot, 0.1-0.5 μg/mL
    Direct ELISA, 0.1-0.5 μg/mL

    Restrictions
    For Research Use only
  • Format
    Lyophilized
    Reconstitution
    Add 0.2 mL of distilled water will yield a concentration of 500 μg/mL.
    Buffer
    Each vial contains 4 mg Trehalose, 0.9 mg NaCl, 0.2 mg Na2HPO4, 0.05 mg NaN3.
    Agent conservateur
    Sodium azide
    Précaution d'utilisation
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Stock
    4 °C,-20 °C
    Stockage commentaire
    At -20°C for one year. After reconstitution, at 4°C for one month.
    It can also be aliquotted and stored frozen at -20°C for a longer time. Avoid repeated freezing and thawing.
  • Antigène
    GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
    Autre désignation
    GNS (GNS Produits)
    Synonymes
    anticorps G6S, anticorps 2610016K11Rik, anticorps AU042285, anticorps C87209, anticorps N28088, anticorps NV14559, anticorps N-acetylglucosamine-6-sulfatase, anticorps zgc:114066, anticorps gns, anticorps wu:fi20h10, anticorps zgc:55370, anticorps glucosamine (N-acetyl)-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase S homeolog, anticorps glucosamine (N-acetyl)-6-sulfatase a, anticorps N-acetylglucosamine-6-sulfatase, anticorps glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b, anticorps GNS, anticorps Gns, anticorps gns.S, anticorps gns, anticorps gnsa, anticorps CpipJ_CPIJ000745, anticorps Sros_7372, anticorps VDBG_04409, anticorps Halhy_3165, anticorps gnsb
    Sujet

    Synonyms: N-acetylglucosamine-6-sulfatase, Glucosamine-6-sulfatase, G6S, GNS

    Background: N-acetylglucosamine-6-sulfatase, also known as glucosamine (N-acetyl)-6-sulfatase, is an enzyme that in humans is encoded by the GNS gene. The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.

    UniProt
    P15586
    Pathways
    Glycosaminoglycan Metabolic Process
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