TIMM8A/DDP anticorps
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- Antigène Voir toutes TIMM8A/DDP (TIMM8A) Anticorps
- TIMM8A/DDP (TIMM8A) (Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))
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Reactivité
- Humain, Souris
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp TIMM8A/DDP est non-conjugé
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Application
- Western Blotting (WB)
- Purification
- Affinity purification
- Immunogène
- Recombinant protein of human TIMM8A
- Isotype
- IgG
- Top Product
- Discover our top product TIMM8A Anticorps primaire
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- Indications d'application
- WB 1:500 - 1:2000
- Restrictions
- For Research Use only
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- Concentration
- 1 mg/mL
- Buffer
- Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
- Agent conservateur
- Sodium azide
- Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Stock
- -20 °C
- Stockage commentaire
- Store at -20°C. Avoid freeze / thaw cycles.
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- Antigène
- TIMM8A/DDP (TIMM8A) (Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))
- Autre désignation
- TIMM8A (TIMM8A Produits)
- Synonymes
- anticorps TIMM8A, anticorps ddp, anticorps tim8a, anticorps timm8a, anticorps DDP, anticorps DDP1, anticorps DFN1, anticorps MTS, anticorps TIM8, anticorps im:6896085, anticorps zgc:100916, anticorps Ddp1, anticorps Timm8a, anticorps DXHXS1274E, anticorps Fci-12, anticorps Tim8a, anticorps translocase of inner mitochondrial membrane 8 homolog A (yeast), anticorps translocase of inner mitochondrial membrane 8A, anticorps translocase of inner mitochondrial membrane 8 homolog A1 (yeast), anticorps translocase of inner mitochondrial membrane 8A1, anticorps TIMM8A, anticorps timm8a, anticorps Timm8a1
- Sujet
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Synonyms: DDP 1,DDP,DDP1,Deafness dystonia protein 1,Deafness/dystonia peptide,DFN 1,DFN1,MGC12262,Mitochondrial import inner membrane translocase subunit Tim8 A,MTS,TIM 8A,TIM8,TIM8A,TIM8A,TIMM 8A,timm8a,Translocase of inner mitochondrial membrane 8 homolog A,X linked deafness dystonia protein,X-linked deafness dystonia protein
Background: This translocase is involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane. The gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS) and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system. Defects in this gene also cause Jensen syndrome, an X-linked disease with opticoacoustic nerve atrophy and muscle weakness. This protein, along with TIMM13, forms a 70 kDa heterohexamer. Alternative splicing results in multiple transcript variants encoding distinct isoforms.
- Poids moléculaire
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Observed_MW: 11kDa
Calculated_MW: 10kDa
- ID gène
- 1678
- UniProt
- O60220
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