IDUA anticorps

N° du produit ABIN7245281

Détail du produit anti-IDUA anticorps

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Reactivité: Humain, Souris

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp IDUA est non-conjugé

Application: ELISA, Immunohistochemistry (IHC)

Attributs du produit: Polyclonal Antibody

Purification: Antigen affinity purification

Immunogène: Synthetic peptide of human IDUA

Isotype: IgG

Information d'application

Indications d'application: IHC 1:30-1:150, ELISA 1:5000-1:10000

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.96 mg/mL

Buffer: PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur IDUA

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Autre désignation: IDUA (IDUA Produits)

Synonymes: anticorps IDA, anticorps MPS1, anticorps 6030426D08, anticorps alpha-L-iduronidase, anticorps MGC80842, anticorps si:ch211-12e13.9, anticorps IDUA, anticorps iduronidase, alpha-L-, anticorps iduronidase, alpha-L- L homeolog, anticorps alpha-L-iduronidase, anticorps IDUA, anticorps Idua, anticorps idua.L, anticorps idua, anticorps LOC5564727

Sujet: This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).

UniProt: P35475

Pathways: Glycosaminoglycan Metabolic Process