ALAS2 anticorps

N° du produit ABIN7262367

Détail du produit anti-ALAS2 anticorps

Antigène: ALAS2 (Aminolevulinate, delta-, Synthase 2 (ALAS2))

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp ALAS2 est non-conjugé

Application: Immunofluorescence (IF)

Attributs du produit: Polyclonal Antibody

Purification: Affinity purification

Immunogène: Recombinant fusion protein of human ALAS2 (NP_001033057.1).

Isotype: IgG

Information d'application

Indications d'application: IF 1:10-1:100

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur ALAS2

Antigène: ALAS2 (Aminolevulinate, delta-, Synthase 2 (ALAS2))

Autre désignation: ALAS2 (ALAS2 Produits)

Synonymes: anticorps anh1, anticorps asb, anticorps xlsa, anticorps ALAS-E, anticorps ALASE, anticorps ANH1, anticorps ASB, anticorps XLDPP, anticorps XLEPP, anticorps XLSA, anticorps alas-e, anticorps cb1063, anticorps sau, anticorps sauternes, anticorps ALAS, anticorps Alas-2, anticorps 5'-aminolevulinate synthase 2, anticorps aminolevulinate, delta-, synthase 2, anticorps aminolevulinic acid synthase 2, erythroid, anticorps alas2, anticorps ALAS2, anticorps Alas2, anticorps alas2.L

Sujet: The product of this gene specifies an erythroid-specific mitochondrially located enzyme. The encoded protein catalyzes the first step in the heme biosynthetic pathway. Defects in this gene cause X-linked pyridoxine-responsive sideroblastic anemia. Alternatively spliced transcript variants encoding different isoforms have been identified.

ID gène: 212

UniProt: P22557

Pathways: Transition Metal Ion Homeostasis