PEX3 anticorps

N° du produit ABIN7263371

Détail du produit anti-PEX3 anticorps

Antigène: PEX3 (Peroxisomal Biogenesis Factor 3 (PEX3))

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp PEX3 est non-conjugé

Application: Immunohistochemistry (IHC)

Attributs du produit: Polyclonal Antibody

Purification: Affinity purification

Immunogène: Recombinant fusion protein of human PEX3 (NP_003621.1).

Isotype: IgG

Information d'application

Indications d'application: IHC 1:50-1:200

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur PEX3

Antigène: PEX3 (Peroxisomal Biogenesis Factor 3 (PEX3))

Autre désignation: PEX3 (PEX3 Produits)

Synonymes: anticorps DDBDRAFT_0204086, anticorps DDBDRAFT_0238047, anticorps DDB_0204086, anticorps DDB_0238047, anticorps zgc:56313, anticorps PBD10A, anticorps TRG18, anticorps Peroxin-3, anticorps 1700014F15Rik, anticorps 2810027F19Rik, anticorps 2900010N04Rik, anticorps peroxisomal biogenesis factor 3, anticorps peroxin 3, anticorps peroxisomal biogenesis factor 3 L homeolog, anticorps LOC692959, anticorps CpipJ_CPIJ013204, anticorps pex3, anticorps PEX3, anticorps pex3.L, anticorps Pex3

Sujet: The product of this gene is involved in peroxisome biosynthesis and integrity. It assembles membrane vesicles before the matrix proteins are translocated. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause Zellweger syndrome (ZWS).

ID gène: 8504

UniProt: P56589