PCCA anticorps

N° du produit ABIN7264805

Détail du produit anti-PCCA anticorps

Antigène: PCCA (Propionyl CoA Carboxylase, alpha Polypeptide (PCCA))

Reactivité: Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp PCCA est non-conjugé

Application: Western Blotting (WB)

Attributs du produit: Polyclonal Antibody

Purification: Affinity purification

Immunogène: Recombinant fusion protein of human PCCA (NP_000273.2).

Isotype: IgG

Information d'application

Indications d'application: WB 1:1000-1:3000

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur PCCA

Antigène: PCCA (Propionyl CoA Carboxylase, alpha Polypeptide (PCCA))

Autre désignation: PCCA (PCCA Produits)

Synonymes: anticorps pcca, anticorps zgc:66359, anticorps C79630, anticorps wu:fb92g02, anticorps zgc:100925, anticorps propionyl-CoA carboxylase alpha subunit, anticorps propionyl-COA carboxylase alpha chain, mitochondrial, anticorps propionyl-CoA carboxylase alpha chain, anticorps zinc finger CCCH-type containing 13, anticorps propionyl-Coenzyme A carboxylase, alpha polypeptide, anticorps propionyl CoA carboxylase, alpha polypeptide, anticorps propionyl-CoA carboxylase alpha subunit L homeolog, anticorps PCCA, anticorps Pcca, anticorps BMEI0800, anticorps pccA, anticorps NRI_0781, anticorps zc3h13, anticorps pcca, anticorps pcca.L

Sujet: The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.

Poids moléculaire:

Observed_MW: 80 kDa

Calculated_MW: 75 kDa/77 kDa/80 kDa

ID gène: 5095

UniProt: P05165

Pathways: Monocarboxylic Acid Catabolic Process