RPGR anticorps (C-Term)

N° du produit ABIN954582

Détail du produit anti-RPGR anticorps

Antigène: RPGR (Retinitis Pigmentosa GTPase Regulator (RPGR))

Épitope: AA 743-772, C-Term

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp RPGR est non-conjugé

Application: Western Blotting (WB), Enzyme Immunoassay (EIA)

Specificité: This antibody reacts to RPGR.

Réactivité croisée (Details): Species reactivity (tested):Human.

Purification: Affinity chromatography on Protein A

Immunogène: KLH conjugated synthetic peptide between 743-772 amino acids from the C-terminal region of human RPGR

Isotype: Ig Fraction

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.25 mg/mL

Buffer: PBS, 0.09 % (W/V) sodium azide

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeated freezing and thawing.

Stock: 4 °C/-20 °C

Stockage commentaire: Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.

Détails sur RPGR

Antigène: RPGR (Retinitis Pigmentosa GTPase Regulator (RPGR))

Autre désignation: RPGR (RPGR Produits)

Synonymes: anticorps xrpgr, anticorps COD1, anticorps CORDX1, anticorps CRD, anticorps PCDX, anticorps RP15, anticorps RP3, anticorps XLRP3, anticorps orf15, anticorps Rp3h, anticorps retinitis pigmentosa GTPase regulator, anticorps retinitis pigmentosa GTPase regulator S homeolog, anticorps Rpgr, anticorps RPGR, anticorps rpgr, anticorps rpgr.S, anticorps Bm1_19935, anticorps NAEGRDRAFT_80250

Sujet: This gene encodes a protein with a series of six RCC1-like domains (RLDs), characteristic of the highly conserved guanine nucleotide exchange factors. The encoded protein is found in the Golgi body and interacts with RPGRIP1. This protein localizes to the outer segment of rod photoreceptors and is essential for their viability. Mutations in this gene have been associated with X-linked retinitis pigmentosa (XLRP). Multiple alternatively spliced transcript variants that encode different isoforms of this gene have been reported, but the full-length natures of only some have been determined.Synonyms: RP3, X-linked retinitis pigmentosa GTPase regulator, XLRP3

Poids moléculaire: 113387 Da

ID gène: 6103

NCBI Accession: NP_000319