SGSH anticorps (C-Term)
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- Antigène Voir toutes SGSH Anticorps
- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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Épitope
- AA 427-457, C-Term
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Reactivité
- Humain
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Hôte
- Lapin
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Clonalité
- Polyclonal
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Conjugué
- Cet anticorp SGSH est non-conjugé
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Application
- Western Blotting (WB), Enzyme Immunoassay (EIA)
- Specificité
- Recognizes Sulphamidase / SGSH (C-term).
- Purification
- Protein A column followed by peptide Affinity purification
- Immunogène
- KLH conjugated synthetic peptide between 427~457 amino acids from the C-terminal region of Human SGSH. Genename: SGSH
- Isotype
- Ig Fraction
- Top Product
- Discover our top product SGSH Anticorps primaire
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- Indications d'application
- Optimal working dilution should be determined by the investigator.
- Restrictions
- For Research Use only
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- Format
- Liquid
- Concentration
- 0.25 mg/mL
- Buffer
- PBS with 0.09 % (W/V) Sodium Azide as preservative
- Agent conservateur
- Sodium azide
- Précaution d'utilisation
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Conseil sur la manipulation
- Avoid repeated freezing and thawing.
- Stock
- 4 °C/-20 °C
- Stockage commentaire
- Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
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- Antigène
- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
- Autre désignation
- Sulphamidase / SGSH (SGSH Produits)
- Synonymes
- anticorps HSS, anticorps MPS3A, anticorps SFMD, anticorps 4632406A19Rik, anticorps N-sulfoglucosamine sulfohydrolase, anticorps N-sulfoglucosamine sulfohydrolase (sulfamidase), anticorps SGSH, anticorps Sgsh
- Sujet
- SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.Synonyms: HSS, N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase
- ID gène
- 6448
- NCBI Accession
- NP_000190
- Pathways
- Glycosaminoglycan Metabolic Process
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