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Fibrillin 1 Produits

(Fibrillin 1 (FBN1))
This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12 nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosynostosis syndrome. [provided by RefSeq, Jul 2008].

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Catégories Fibrillin 1 en vedette

Fibrillin 1 Anticorps

High quality antibodies with extensive validation data.

Fibrillin 1 Kits ELISA

Reliable ELISA kits for a wide range of species.

Fibrillin 1 Protéines

Proteins for various applications incl. WB, ELISA, IF etc.

Fibrillin 1 recommandé Anticorps

Produit
Reactivity
Application
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Application WB, ELISA, ICC, IHC (p), IHC (fro)
Validations
  • (11)
N° du produit ABIN7438742
Quantité 100 μL
Fiche technique Fiche technique
Reactivity Rat
Application WB, IHC, IP, ICC
Validations
  • (7)
N° du produit ABIN7432139
Quantité 100 μL
Fiche technique Fiche technique
Reactivity Human
Application ELISA, IF
Validations
  • (6)
N° du produit ABIN570798
Quantité 100 μg
Fiche technique Fiche technique

Fibrillin 1 recommandé Kits ELISA

Produit
Reactivity
Analytical Method
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (5)
N° du produit ABIN6574170
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Rat
Analytical Method Quantitative Sandwich ELISA
Validations
  • (5)
N° du produit ABIN6574171
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Mouse
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
N° du produit ABIN6955770
Quantité 96 tests
Fiche technique Fiche technique

Fibrillin 1 recommandé Protéines

Produit
Reactivity
Source
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Source Wheat germ
Validations
  • (1)
  • (1)
N° du produit ABIN1353704
Quantité 10 μg
Fiche technique Fiche technique
Reactivity Mouse
Source Human Cells
Validations
  • (1)
N° du produit ABIN7320523
Quantité 50 μg
Fiche technique Fiche technique
Reactivity Mouse
Source Escherichia coli (E. coli)
Validations
N° du produit ABIN3135431
Quantité 1 mg
Fiche technique Fiche technique

Dernières publications sur nos produits Fibrillin 1

Ceylan, Saygın, Özel Türkcü: "Assessment of acute aerobic exercise in the morning versus evening on asprosin, spexin, lipocalin-2, and insulin level in overweight/obese versus normal weight adult men." dans: Chronobiology international, Vol. 37, Issue 8, pp. 1252-1268, (2020) (PubMed).

Bell, Gendron, Anderson, Flatow, Andarawis-Puri: "A potential new role for myofibroblasts in remodeling of sub-rupture fatigue tendon injuries by exercise." dans: Scientific reports, Vol. 8, Issue 1, pp. 8933, (2018) (PubMed).

Shin, Lee, Kim, Kum, Jung, Park: "Anti-glycation activities of phenolic constituents from Silybum marianum (Milk Thistle) flower in vitro and on human explants." dans: Molecules (Basel, Switzerland), Vol. 20, Issue 3, pp. 3549-64, (2015) (PubMed).

Shin, Son, Kim, Lee, Roh, Ryu, Lee, Jung, Park: "Ameliorating Effect of Akebia quinata Fruit Extracts on Skin Aging Induced by Advanced Glycation End Products." dans: Nutrients, Vol. 7, Issue 11, pp. 9337-52, (2015) (PubMed).

Zhang, Ota, Shridhar, Chien, Wu, Kuang: "Network-based survival analysis reveals subnetwork signatures for predicting outcomes of ovarian cancer treatment." dans: PLoS computational biology, Vol. 9, Issue 3, pp. e1002975, (2013) (PubMed).

Baldwin, Cain, Lennon, Godwin, Merry, Kielty: "Epithelial-mesenchymal status influences how cells deposit fibrillin microfibrils." dans: Journal of cell science, Vol. 127, Issue Pt 1, pp. 158-71, (2013) (PubMed).

Edlund, Lindskog, Saito, Berglund, Pontén, Göransson-Kultima, Isaksson, Jirström, Planck, Johansson, Lambe, Holmberg, Nyberg, Ekman, Bergqvist, Landelius, Lamberg, Botling, Ostman, Micke: "CD99 is a novel prognostic stromal marker in non-small cell lung cancer." dans: International journal of cancer, Vol. 131, Issue 10, pp. 2264-73, (2012) (PubMed).

Atanasova, Konova, Aleksovska, Todorova, Georgieva, Lukanov: "Anti-fibrillin-1 autoantibodies in normal pregnancy and recurrent pregnancy loss." dans: Autoimmunity reviews, Vol. 10, Issue 3, pp. 131-6, (2011) (PubMed).

Morisaki, Akutsu, Ogino, Kondo, Yamanaka, Tsutsumi, Yoshimuta, Okajima, Matsuda, Minatoya, Sasaki, Tanaka, Ishibashi-Ueda, Morisaki: "Mutation of ACTA2 gene as an important cause of familial and nonfamilial nonsyndromatic thoracic aortic aneurysm and/or dissection (TAAD)." dans: Human mutation, Vol. 30, Issue 10, pp. 1406-11, (2009) (PubMed).

Synonymes et noms alternatifs relatifs à Fibrillin 1

fibrillin 1 (FBN1), fibrillin 1 (Fbn1), ACMICD, AI536462, B430209H23, ECTOL1, FBN, FBN1, Fib-1, GPHYSD2, MASS, MFS1, OCTD, SGS, SSKS, Tsk, WMS, WMS2

Protein level used designations for Fibrillin 1

  • fibrillin 1
  • MP340
  • fibrillin-1
  • fibrillin 15
  • fibrillin 1 (Marfan syndrome)
  • tight skin
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