GBE1 Produits
(Glucan (1,4-alpha-), Branching Enzyme 1 (GBE1))
Catégories
The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease). [provided by RefSeq, Jul 2008].
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Catégories GBE1 en vedette
GBE1 Anticorps
High quality antibodies with extensive validation data.
GBE1 Kits ELISA
Reliable ELISA kits for a wide range of species.
GBE1 Protéines
Proteins for various applications incl. WB, ELISA, IF etc.
GBE1 recommandé Anticorps
Produit
Reactivity
Application
Validations
N° du produit
Quantité
Fiche technique
Reactivity
Human
Application
WB, IHC, IP, FACS, IHC (p)
Validations
- (9)
N° du produit
ABIN1498396
Quantité
100 μL
Fiche technique
Fiche technique
Reactivity
Human
Application
WB, IF, IP, FACS
Validations
- (4)
N° du produit
ABIN1498395
Quantité
100 μL
Fiche technique
Fiche technique
Reactivity
Human, Mouse
Application
WB, IF
Validations
- (3)
N° du produit
ABIN653459
Quantité
400 μL
Fiche technique
Fiche technique
GBE1 recommandé Kits ELISA
Produit
Reactivity
Analytical Method
Validations
N° du produit
Quantité
Fiche technique
Reactivity
Human
Analytical Method
Quantitative Competition ELISA
Validations
N° du produit
ABIN1742631
Quantité
96 tests
Fiche technique
Fiche technique
Reactivity
Sheep
Analytical Method
Validations
N° du produit
ABIN1773535
Quantité
96 tests
Fiche technique
Fiche technique
Reactivity
Pig
Analytical Method
Validations
N° du produit
ABIN1749960
Quantité
96 tests
Fiche technique
Fiche technique
GBE1 recommandé Protéines
Produit
Reactivity
Source
Validations
N° du produit
Quantité
Fiche technique
Reactivity
Human
Source
Wheat germ
Validations
- (1)
N° du produit
ABIN1354871
Quantité
10 μg
Fiche technique
Fiche technique
Reactivity
Human
Source
Wheat germ
Validations
- (1)
N° du produit
ABIN1354873
Quantité
10 μg
Fiche technique
Fiche technique
Reactivity
Human
Source
HEK-293 Cells
Validations
- (1)
N° du produit
ABIN2721752
Quantité
20 μg
Fiche technique
Fiche technique
Dernières publications sur nos produits GBE1
: "Adult polyglucosan body disease: clinical and histological heterogeneity of a large Italian family." dans: Neuromuscular disorders : NMD, Vol. 25, Issue 5, pp. 423-8, (2015) (PubMed).: "Muscle glycogen remodeling and glycogen phosphate metabolism following exhaustive exercise of wild type and laforin knockout mice." dans: The Journal of biological chemistry, (2015) (PubMed).
: "A novel mouse model that recapitulates adult-onset glycogenosis type 4." dans: Human molecular genetics, Vol. 24, Issue 23, pp. 6801-10, (2015) (PubMed).
: "Polyglucosan neurotoxicity caused by glycogen branching enzyme deficiency can be reversed by inhibition of glycogen synthase." dans: Journal of neurochemistry, Vol. 127, Issue 1, pp. 101-13, (2013) (PubMed).
: "Generation of a novel mouse model that recapitulates early and adult onset glycogenosis type IV." dans: Human molecular genetics, Vol. 20, Issue 22, pp. 4430-9, (2011) (PubMed).
Synonymes et noms alternatifs relatifs à GBE1
1,4-alpha-glucan branching protein GlgB (glgB), 1,4-alpha-glucan branching protein (glgB), glycogen branching protein (ECs4277), glycogen branching protein (glgB), glycogen branching enzyme (glgB), 1,4-alpha-glucan-branching protein (SCO7332), glycogen branching enzyme; BE; 1,4-alpha-D-glucan:1,4-alpha-D-glucan 6-glucosyl-transferase (glgB), glycogen branching enzyme (Synpcc7942_1085), glycogen branching enzyme (AZC_4116), glycogen branching enzyme (Sros_8169), glycogen branching enzyme (Despr_0975), 1,4-alpha-glucan branching enzyme 1 (GBE1), glucan (1,4-alpha-), branching enzyme 1 (Gbe1), 1,4-alpha-glucan branching enzyme 1 (Gbe1), 2310045H19Rik, 2810426P10Rik, APBD, D16Ertd536e, GBE, glgBII, GSD4Protein level used designations for GBE1
- glycogen branching enzyme
- 1,4-alpha-glucan-branching enzyme
- amylo-(1,4 to 1,6) transglucosidase
- amylo-(1,4 to 1,6) transglycosylase
- brancher enzyme
- glycogen-branching enzyme
- glucan (1,4-alpha-), branching enzyme 1 (glycogen branching enzyme, Andersen disease, glycogen storage disease type IV)
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