GLA Produits
(Galactosidase, alpha (GLA))
Catégories
This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008].
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Catégories GLA en vedette
GLA Anticorps
High quality antibodies with extensive validation data.
GLA Kits ELISA
Reliable ELISA kits for a wide range of species.
GLA Protéines
Proteins for various applications incl. WB, ELISA, IF etc.
GLA recommandé Anticorps
Produit
Reactivity
Application
Validations
N° du produit
Quantité
Fiche technique
Reactivity
Human
Application
WB, IHC, IP, ICC
Validations
- (7)
N° du produit
ABIN7431278
Quantité
100 μL
Fiche technique
Fiche technique
Reactivity
Human
Application
WB, IHC, IP, ICC
Validations
- (6)
N° du produit
ABIN7426817
Quantité
100 μL
Fiche technique
Fiche technique
Reactivity
Human
Application
WB, IP, IHC (p)
Validations
- (2)
- (5)
N° du produit
ABIN2854962
Quantité
100 μL
Fiche technique
Fiche technique
GLA recommandé Kits ELISA
Produit
Reactivity
Analytical Method
Validations
N° du produit
Quantité
Fiche technique
Reactivity
Human
Analytical Method
Quantitative Sandwich ELISA
Validations
- (5)
N° du produit
ABIN6720556
Quantité
96 tests
Fiche technique
Fiche technique
Reactivity
Human
Analytical Method
Quantitative Sandwich ELISA
Validations
- (1)
N° du produit
ABIN3199196
Quantité
96 tests
Fiche technique
Fiche technique
Reactivity
Mouse
Analytical Method
Quantitative Sandwich ELISA
Validations
N° du produit
ABIN6730640
Quantité
96 tests
Fiche technique
Fiche technique
GLA recommandé Protéines
Produit
Reactivity
Source
Validations
N° du produit
Quantité
Fiche technique
Reactivity
Human
Source
Wheat germ
Validations
- (1)
- (1)
N° du produit
ABIN1355176
Quantité
10 μg
Fiche technique
Fiche technique
Reactivity
Human
Source
Escherichia coli (E. coli)
Validations
- (1)
N° du produit
ABIN7123037
Quantité
50 μg
Fiche technique
Fiche technique
Reactivity
Mouse
Source
HEK-293 Cells
Validations
- (1)
N° du produit
ABIN7320092
Quantité
50 μg
Fiche technique
Fiche technique
Dernières publications sur nos produits GLA
: "Rapid Clathrin-Mediated Uptake of Recombinant α-Gal-A to Lysosome Activates Autophagy." dans: Biomolecules, Vol. 10, Issue 6, (2020) (PubMed).: "Ligand-promoted protein folding by biased kinetic partitioning." dans: Nature chemical biology, Vol. 13, Issue 4, pp. 369-371, (2017) (PubMed).
: "Comparison of intracellular and secretion-based strategies for production of human ?-galactosidase A in the filamentous fungus Trichoderma reesei." dans: BMC biotechnology, Vol. 14, pp. 91, (2015) (PubMed).
: "Coformulation of a Novel Human α-Galactosidase A With the Pharmacological Chaperone AT1001 Leads to Improved Substrate Reduction in Fabry Mice. ..." dans: Molecular therapy : the journal of the American Society of Gene Therapy, Vol. 23, Issue 7, pp. 1169-81, (2015) (PubMed).
: "Establishing 3-nitrotyrosine as a biomarker for the vasculopathy of Fabry disease." dans: Kidney international, Vol. 86, Issue 1, pp. 58-66, (2014) (PubMed).
: "A thermodynamic assay to test pharmacological chaperones for Fabry disease." dans: Biochimica et biophysica acta, Vol. 1840, Issue 3, pp. 1214-24, (2014) (PubMed).
: "Integrated approach to produce a recombinant, His-tagged human ?-galactosidase A in mammalian cells." dans: Biotechnology progress, Vol. 27, Issue 5, pp. 1206-17, (2011) (PubMed).
: "Protein translocation: how Hsp70 pulls it off." dans: Cell, Vol. 97, Issue 6, pp. 679-82, (1999) (PubMed).
: "The Hsp70 and Hsp60 chaperone machines." dans: Cell, Vol. 92, Issue 3, pp. 351-66, (1998) (PubMed).
: "Expression of hsp70 induced in CHO cells by 45.0 degrees C hyperthermia is cell cycle associated and DNA synthesis dependent." dans: Cytometry, Vol. 19, Issue 2, pp. 119-25, (1995) (PubMed).
Synonymes et noms alternatifs relatifs à GLA
galactosidase alpha (GLA), galactosidase, alpha (Gla), galactosidase, alpha (gla), galactosidase alpha S homeolog (gla.S), galactosidase alpha (gla), alpha-galactosidase (agaN), aga (aga), alpha-galactosidase (agaL), alpha-galactosidase (SCO0541), alpha-galactosidase (rafA), alpha-galactosidase (melA), alpha-galactosidase (galA), alpha-galactosidase A (ANI_1_2528074), alpha-galactosidase A (ANI_1_1502124), alpha-galactosidase A (AOR_1_390174), alpha-galactosidase A (CpipJ_CPIJ002066), alpha-galactosidase (aga), alpha-galactosidase A (MCYG_00962), alpha-galactosidase A (MCYG_00791), alpha-galactosidase (gla), alpha-galactosidase A (Tsp_02909), alpha-galactosidase A (Tsp_02508), galactosidase alpha (Gla), galactosidase, alpha (GLA), Ags, alpha-GAL, AO090005000217, GALA, MGC130872, SCF11.21, SMU.877, zgc:101584Protein level used designations for GLA
- agalsidase alfa
- alpha-D-galactosidase A
- alpha-D-galactoside galactohydrolase 1
- alpha-gal A
- alpha-galactosidase A
- melibiase
- alpha-D-galactoside galactohydrolase
- Alpha-galactosidase A
- galactosidase, alpha
- alpha-galactosidase A-like
- alpha-galactosidase
- Alpha-galactosidase
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